Moderate PI*Mmalton N = 26 | Severe PI*Mmalton N = 33 | PI*ZZ N = 827 | P-value1 | ||||
---|---|---|---|---|---|---|---|
Age of onset of symptoms, mean ± SD | 43.9 | ± 19.7 | 47.6 | ± 14.8 | 43.3 | ± 15.6 | 0.406 |
Age of diagnosis (AATD), mean ± SD | 46.3 | ± 18.7 | 48.6 | ± 15.7 | 45.9 | ± 16.9 | 0.662 |
Alpha- 1 antitrypsin levels (mg/dl), Median (IQR) | 54 | (48–2277) | 25 | (20–29) | 24 | (18–97) | 0.191 |
Patients under Augmentation Therapy, n (%) | 4* | (15.4%) | 14β | (45.2%) | 288 | (35.2%) | 0.054 |
Age at the beginning of Augmentation Therapy, mean \(\pm\) SD | 65.3 | ± 11.5 | 53.7 | ± 13.8 | 55.3 | ± 11.1 | 0.185 |
Number of years after diagnosis, median (IQR) | 3 | (1–8) | 1 | (0–2) | 2 | (1–8) | 0.152 |